Carcinoma basoescamoso mutilante en región facial / Facial mutilant basosquamous carcinoma

El carcinoma basoescamoso constituye una neoplasia epithelial maligna poco frecuente, que comparte características clínicas y biológicas con el carcinoma basocelular y espinocelular. Esta neoplasia ha sido considerada durante años una variedad de carcinoma basocelular, aunque en la actualidad se acepta plenamente su entidad propia. Presentamos el caso de un varón de 59 años de edad, indigente, que presentaba lesión tumoral ulcerada, de cuatro años de evolución, localizada en región malar izquierda, orbitaria y pirámide nasal, con importante destrucción de estas estructuras y extensión a la base del cráneo a través del nervio óptico. La importancia del carcinoma basoescamoso radica en su gran agresividad local, tendencia a la recidiva y capacidad de producir metástasis a distancia, por lo que el tratamiento más efectivo es la detección precoz y extirpación completa del mismo; hecho, que como ocurre en el caso que presentamos, no es siempre posible

Basosquamous carcinoma is a rare epithelial malignant neoplasm with clinical and biological features of both basal and squamous cell carcinoma. This neoplasm has been characterized for years as a variant of basal cell carcinoma, although now it is widely accepted as a clinical entity. We report a 59-year-old male patient, homeless, who presented an ulcerated tumoral lesion from four years ago, located in left malar region, orbit and nasal pyramid. It caused an important destruction of these anatomic structures and spred out the skull base through optic nerve. The most important features of basosquamous carcinoma are its great local aggressiveness, high frequency of recurrences and its metastatic potential. Because of that, the most effective therapeutic measure is the early detection and complete removement of these tumours; although, as the case we report, it is not always possible

[Schwannomas of the lingual nerve]. / Schwanoma del nervio lingual.

Schwanomas in extracranial head and neck region are an uncommon tumour, but when refered to its origin in the parasympathetic nerve fibers are extremely rare. We describe a case of schwanoma of the right submandibular gland originating from the parasympathetic branch of the lingual nerve, and we discuss about the clinical, diagnostic and therapeutic aspects of this rare tumour and a literature review of the recent cases.

Schwannoma del nervio lingual / Schwannomas of the lingual nerve

Los schwannomas de cabeza y cuello extracraneales constituyen una variedad tumoral relativamente infrecuente, pero cuando hablamos de su origen en las fibras parasimpáticas del nervio lingual se convierten en algo excepcional. Presentamos un caso de schwanoma de la región submandibular derecha originado en las ramas parasimpáticas que el nervio lingual proporciona a la glándula submaxilar, realizando una discusión acerca de los aspectos clínicos, diagnósticos y terapéuticos de esta variedad tumoral y una revisión de los casos descritos en la literatura médica reciente

Schwanomas in extracranial head and neck region are an uncommon tumour, but when refered to its origin in the parasympathetic nerve fibers are extremely rare. We describe a case of schwanoma of the right submandibular gland originating from the parasympathetic branch of the lingual nerve, and we discuss about the clinical, diagnostic and therapeutic aspects of this rare tumour and a literature review of the recent cases

[Nasoalveolar cyst. Five new cases]. / Quistes nasoalveolares. Presentación de 5 nuevos casos.

Nasoalverolar cyst are nonodontogenic maxillary cysts, rare and benign, which are more common in females and blacks. Their diagnosis can be established mainly on the clinical presentation, being usually asymptomatic during several years until they are large enough to cause cosmetic deformities and/or nasal obstruction, with asymmetrical alar flare. The treatment of choice is the complete surgical excision via a sublabial approach. Five cases diagnosed and treated at the Santa Maria del Rosell Hospital are reported, describing the most relevant clinican and pathological findings, so the diagnostic ant therapeutic methods.

Quistes nasoalveolares. Presentación de 5 nuevos casos / Nasoalveolar cyst. Five new cases

Inverted papilloma is a benign sinonasal tumour with a high recurrence rate and its treatment must be surgery, using endonasal surgery or external aproach. We present a retrospective study of 23 cases treated in our center from 1988 to 2003. There 15 males and 8 females with a mean follow-up of 6 years. The recurrence rate was 40,9%. Patients who underwent endonasal surgery had a recurrence rate of 36,6% and those who underwent external approach surgery had a recurrence rate of 45,5%. There was a 4,5% of association with carcinoma. Endonasal surgery might be a valid surgery approach for the treatement of inverted papilloma in select cases

Nasoalveolar cyst are nonodontogenic maxillary cysts, rare and benign, which are more common in females and blacks. Their diagnosis can be established mainly on the clinical presentation, being usually asymptomatic during several years until they are large enough to cause cosmetic deformities and/or nasal obstruction, with asummetrical alarflare. The treatment of choice is the complete surgical excision via a sublabial approach. Five cases diagnosed an treated at the Santa María del Rosell Hospital are reported, describing the most relevant clinican and pathological findings, so the diagnostic and therapeutic methods

[Facial mutilant basosquamous carcinoma]. / Carcinoma basoescamoso mutilante en región facial.

Basosquamous carcinoma is a rare epithelial malignant neoplasm with clinical and biological features of both basal and squamous cell carcinoma. This neoplasm has been characterized for years as a variant of basal cell carcinoma, although now it is widely accepted as a clinical entity. We report a 59-year-old male patient, homeless, who presented an ulcerated tumoral lesion from four years ago, located in left malar region, orbit and nasal pyramid. It caused an important destruction of these anatomic structures and spred out the skull base through optic nerve. The most important features of basosquamous carcinoma are its great local aggressiveness, high frequency of recurrences and its metastatic potential. Because of that, the most effective therapeutic measure is the early detection and complete removement of these tumours; although, as the case we report, it is not always possible.

Agenesia de la supraestructura del estribo / Congenital absence of the stapes suprastructure

La ausencia de la supraestructura del estribo es una anomalía congénita muy rara, secundaria a un desarrollo aberrante del segundo arco branquial con ausencia parcial de las estructuras derivadas de él. En la mayoría de las ocasiones, su diagnóstico es casual en una timpanotomía exploradora realizada ante una hipoacusia de transmisión de origen incierto. Puede aparecer de forma aislada o asociada a otras anomalías mayores o menores. El tratamiento es quirúrgico. Realizamos una revisión de la literatura existente, a propósito de un caso de ausencia de la supraestructura del estribo aislada

Congenital absence of the stapes suprastructure is an unusual anomaly, consequence of a developmental aberration involving partial absence of a derivate from the second branchial arch. Sometimes, exploratory tympanotomy may be the only mean of diagnosis when known conductive hearing loss is seen. This anomaly can appear isolated or associated to other major or minor anomalies. The treatment is surgical. We review the literature about the absence of the isolated stapes suprastructure

[Congenital absence of the stapes suprastructure]. / Agenesia de la supraestructura del estribo.

Congenital absence of the stapes suprastructure is an unusual anomaly, consequence of a developmental aberration involving partial absence of a derivate from the second branchial arch. Sometimes, exploratory tympanotomy may be the only mean of diagnosis when known conductive hearing loss is seen. This anomaly can appear isolated or associated to other major or minor anomalies. The treatment is surgical. We review the literature about the absence of the isolated stapes suprastructure.